Authors : Anusha R. L, Anusha R. L, Shruti R. L, Shruti R. L, Sham Kishor K, Sham Kishor K, Chaithra K, Chaithra K, Nilofer Halim, Nilofer Halim
DOI : 10.18231/j.ijmi.2019.012
Volume : 5
Issue : 2
Year : 2019
Page No : 44-46
Hereditary sensory and autonomic neuropathy type IV or Congenital insensitivity to pain with anhydrosis is a rare autosomal recessive disorder. It is characterized by absence of small myelinated and unmyelinated sympathetic nerves resulting in pain and temperature insensitivity. We report a case of a 15 year old boy with hereditary sensory and autonomic neuropathy type IV associated with bifid tongue which is an extremely rare oral presentation and not often reported in literature.
Keywords: Hereditary sensory and autonomic neuropathy type IV, Bifid tongue, Self mutilation.