Authors : Gunjan Chadha, Medha Sharma, Arvind Chauhan
DOI : 10.18231/j.ijceo.2021.118
Volume : 7
Issue : 3
Year : 2021
Page No : 599-601
Purpose: To report a case on unusual presentation of Axenfeld Reiger (A-R) syndrome.
Observation: Axenfeld Rieger syndrome commonly presents with prominent Schwalbe’s line near the limbus. Presentation with displaced Schwalbe’s line is rarely reported. We report 2 cases who presented with bilaterally displaced Schwalbe ring as strange cord like structure in anterior chamber with iris tissue adhesions.
Conclusion: Axenfeld – Reiger syndrome is an autosomal dominant disease with ocular findings involving cornea (megalocornea), iris (iris atrophy,correctopia) and angle (anterior insertion of iris, prominent Schwalbe line). We report unsual case of detached Schwalbe’s line with iris tissue adhesions in anterior chamber A-R syndrome.
Keywords: Axenfeld rieger syndrome, Schwalbe’s line.