Authors : Radhika C. Sasturkar, Amaresh Deginal, Prabhu M. H
DOI : 10.18231/j.jdpo.2019.033
Volume : 4
Issue : 2
Year : 2019
Page No : 156-158
Primitive neuroectodermal tumors (PNETs) are malignant soft tissue tumors of uncertain origin. They usually occur in the deep soft tissues. PNET of the spine are rare. We herein report a case of PNET occurring in thoracic region in an adult male. A 44-year-old male presented with acute onset lower extremity weakness and urinary retention. Magnetic resonance imaging revealed a mass lesion well defined moderately homogenously enhancing extradural lesion at D6. D7 and D8 level, extending into bony spinal canal and left neural foramina causing their widening at D6 and D7 level. On examination patient was conscious and oriented, higher mental functions are normal, cranial nerves normal. Paraplegia was seen with bowel and bladder fully involved. There was no sensation below D6 level. Deep tendon reflexes were absent. The patient’s neurological examination improved dramatically after the surgery. The histopathological and immunohistochemical evaluations revealed PNET. Surgery remains the treatment of choice and immunohistochemistry is required for confirming the diagnosis.
Keywords: Primitive neuroectodermal tumor, Extradural, Thoracic region, Paraplegia.