Acantholytic dyskeratotic epidermal nevus which mimic as a darier’s disease

Darier’s disease is characterized by multiple hyperkeratotic lesions and crusted papules or plaques involving seborrheic areas along with palmoplantar pits, and nail changes. Epidermal naevus may show acantholytic histology similar to darier's disease. Presenting a case of acantholytic dyskeratotic epidermal nevus mimicking darier’s disease. Negative family history, no significant signs of darier’s disease with limited distribution of lesions favour a nevoid origin.

Keywords: Darier’s disease, Epidermal naevus, Retinoids.