Authors: Shweta Dhiman, Kavita Rani Sharma
Klippel feil syndrome is a rare skeletal disorder primarily characterized by abnormal union or fusion of two or more cervical vertebrae which is often associated with cervical canal stenosis. This results in a short neck, a low hairline at the back of the head, a limited range of motion in the neck and infrequently an atlanto- axial instability. Here we report a case of type 3 paediatric Klippel Feil syndrome who underwent Sprengel deformity repair in prone position and its anesthetic implications. A careful assessment of airway and an algorithmic approach towards management is needed in children with KFS. The various spine deformities associated with KFS demand careful positioning and a reconfirmation of appropriate ETT position, airway pressures and lung compliance is recommended in these children. Keywords: Klippel Feil syndrome, Paediatric, Airway management, Prone positioning, Difficult airway.
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