Madhusmita Behera

Abstract

Papillary oncocytoma is an uncommon tumor arising within the ductular cell lining of glandular structures. These tumors contain transformed epithelial cells with eosinophilic granular cytoplasm containing densely packed abnormal mitochondrias. Ocular oncocytomas are usually benign in nature, but occasionally there can be malignant transformation, with both local and distant spread. We are reporting a case of papillary oncocytoma, who was managed with surgery without any recurrence on follow up. Keywords: Oxyphil adenomas, Papillary oncocytoma.

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Abstract

Bardet-Biedl syndrome (BBS) is a rare autosomal recessive disorder with wide spectrum of clinical features. BBs is distinguished from the much rarer Laurence-moon syndrome, in which retinal pigmentary degeneration, mental retardation, and hypogonadism occur in association with progressive spastic paraparesis and distal muscle weakness, but without polydactyly. Most common feature of BBS is retinal dystrophy. The visual prognosis for children with Bardet-Biedl syndrome is poor. Keywords: Mental retardation, Pigmentary retinopathy, Polydactyly.

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