An audiological profile in vogt-koyanagi-harada syndrome

The Vogt-Koyanagi-Harada syndrome (VKHS) is a rare, multisystemic, granulomatous inflammatory and autoimmune disease that affects the pigmented structures such as eyes, ears, skin, and hair. The syndrome mainly affects the eyes, followed by bilateral chronic panuveitis. A 34 years old female came with complaints of reduced vision and reduced hearing sensitivity to our hospital. She was diagnosed with VKHS in the ophthalmology department. Throughout the audiologist assessment, she presented bilateral sensorineural hearing loss, absent otoacoustic evoked emissions, and complaints about postural vertigo and acute tinnitus. The specific case reported presented sudden sensorineural hearing loss, vertigo, tinnitus, and bilateral ocular disease. Even though drug treatment was performed, the hearing loss remained.


Keywords: Auditory brain stem response instead of Yoshizo Koyanagi, Otoacoustic emission, Auditory Brain stem response, VKH syndrome